Investigating the Prevalence of Congenital Heart Disease in Imperforate Anus Infants Referred To Pediatric Surgery Department of Dr. Sheikh Hospital in Mashhad Iran

Document Type : Original Article


1 M.Sc. of Nursing, Department of Nursing, Islamic Azad University of Quchan, Quchan, Iran

2 M.Sc. of Psychology, Mashhad University of Medical Sciences, Mashhad, Iran.

3 Associate professor and Subspecialist of pediatric surgery, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran.


Introduction: Imperforate anus (IA) is a congenital abnormality in which the baby cannot excrete feces normally. The infant is born without a normal rectal opening. This disorder is the most common pediatric surgical problem. Since imperforate anus patients are operated in the first few days of infancy, diagnosis of other congenital anomalies is of vital importance. The present study was aimed to determine the prevalence of congenital heart disease in patients with imperforate anus.
Methods: This retrospective-descriptive study was held on 97 patients with imperforate anus who were referred to Dr. Sheikh Pediatric hospital for surgery and were undergone echocardiography (2004-2009). Information about congenital heart anomalies and its type, infant's gender, and age of mothers were recorded. Finally, overall prevalence of heart disease risk and affliction to its different types were measured and reported. Data were analyzed by SPSS statistical software version 14. In order to compare mothers' age in cardiac and non-cardiac infants, T-test was used. And chi-square test was performed to compare the infants' gender in two groups.
Results: No cardiac dysfunction was observed in 68 infants (70%) while 29 (30%) of them had congenital heart anomalies. 16 infants (55%) were male and 13 infants (45%) were female. The highest prevalence rate of congenital heart anomalies was in the Northern Khorasan. The most common congenital heart diseases were respectively: Atrial septal defect (45%), ventricular septal defect (27.5%), ventricular septal defect with patent ductus arteriosus (10/3%), and ventricular septal defect with atrial septal defect (7%), and patent ductus arteriosus with atrial septal defect (3.4%), patent ductus arteriosus with ventricular septal defect and atrial septal defect (3.4%) and tetralogy of fallot (3.4%).
Conclusion: This study confirms an increased risk of congenital heart disease among infants with imperforate anus.


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