A Case Report of Budd-Chiari Syndrome with HELLP Syndrome Symptoms

Document Type : Case report

Authors

1 Assistant Professor, Department of Obstetrics and Gynecology, Health Services Research Center of Obstetrics, School of Medicine, Kermanshah University of Medical Sciences, Kermanshah, Iran.

2 M.Sc. of Biochemistry, School of Pharmacy, Kermanshah University of Medical Sciences, Kermanshah, Iran.

3 Associate Professor, Department of Internal Medicine, School of Medicine, Kermanshah University of Medical Sciences, Kermanshah, Iran.

Abstract

Introduction: Budd-Chiari Syndrome is a rare disease primarily determined by the hepatic veins thrombosis. Spontaneous thrombosis of the hepatic veins is the main reason, but polycythemia vera and a history of using oral contraceptive pills can be associated with thrombosis. Some patients refer with idiopathic membranous obstruction of the inferior vena cava at the distance between hepatic veins and right atrium which is usually associated with hepatic vein thrombosis of one or both hepatic veins. Initially it was thought that these lesions are congenital, but it is now clear that these lesions result from stenosis due to thrombosis and scar formation. Obstruction after the liver increases sinusoids pressure and eventually portal vein hypertension occurs. Symptoms are usually mild and general at first and include abdominal pain of the right upper quadrant, bloating and anorexia. After a few weeks or months, clinical manifestations presented as sever fever, clinical ascites, hepatomegaly and hepatic necrosis. Venography is one of the ways of diagnosis.
Case Report: A 22 years old woman is reported with Budd-Chiari syndrome which started after delivery. The patient was considered following the cesarean section because of ascites symptoms, high fever and high blood pressure due to delays in diagnosis.
After conducting ultrasonography and liver biopsy simultaneously, hepatic vein thrombosis was reported and Budd-Chiari syndrome was diagnosed.

Keywords

References

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